52.
Maple syrup urine disease, leading to characteristic smell in urine is due to defect in which of the following pathways;
A:
Defect in the catabolism of branched chain amino acid
B:
Defect in anabolism of branched chain amino acid
C:
Defect in catabolism of aromatic amino acid
D:
Defect in anabolism of aromatic amino acid
The answer is:
A